What is meningeal hemangiopericytoma?

What is meningeal hemangiopericytoma?

Meningeal hemangiopericytoma is a rare neoplasm arising from perivascular pericytes. Accounting for < 1% of all brain tumors, these neoplasms are characterized by a high local recurrence rate and metastatic potential.

Is hemangiopericytoma malignant?

Hemangiopericytomas can be either benign (non-cancerous) or malignant (cancerous). Malignant hemangiopericytomas can metastasize or spread to other areas in the body, primarily the lungs and bones. Hemangiopericytomas can be located in the nasal cavity and paranasal sinuses.

Is hemangiopericytoma a soft tissue sarcoma?

Hemangiopericytoma (HPC) is a rare disease entity of soft tissue sarcomas that originates in the pericytes in the walls of capillaries, and was first described in 1942 by Arthur Purdy Stout and Margaret R. Murray. They have a high propensity for recurrence (1).

What is hemangiopericytoma like pattern?

Hemangiopericytoma (HPC) is an uncommon neoplasm characterized by a dense, blunt spindle-cell proliferation with a richly vascular stroma. Supporting blood vessels often assume a staghorn configuration.

What causes Hemangiopericytoma?

What causes hemangiopericytoma? While the cause is unknown, genetic changes have been associated with some soft tissue sarcomas and there may be some relationship to certain environmental exposures such as herbicides or vinyl chloride.

What is anaplastic Hemangiopericytoma?

Intracranial anaplastic hemangiopericytoma (AHPC) is a rare and malignant subset of solitary fibrous tumor/hemangiopericytoma (SFT/HPC) as per the WHO 2016 Classification of Tumors of the Central Nervous System.

What causes hemangiopericytoma?

What is anaplastic hemangiopericytoma?

How long can a dog live with hemangiopericytoma?

The median survival time for dogs with these types of tumors is 2-4 years. High-grade tumors have a much lower survival time of 49 weeks, but these types of tumor are less common.

What is metastatic hemangiopericytoma?

Hemangiopericytoma is a rare disease entity of soft-tissue sarcoma (STS) that can be cured with surgical resection. In cases of inoperable recurrence or metastasis, palliative chemotherapy is indicated, though there is currently no approved chemotherapy regimen. Therefore new treatment regimens are needed.

Is hemangiopericytoma hereditary?

What is central nervous system hemangiopericytoma?

Central nervous system (CNS) hemangiopericytoma (HPC) is a rare mesenchymal tumor which was first described by Stout and Murray [1] in 1942. HPC accounts for 2.5% of all meningeal tumors and <1% of all CNS tumors [2,3,4].

What is the treatment for meningeal hemangiopericytoma?

Treatment Treatment. Radical surgical resection with removal of all meningeal attachments is typically the preferred treatment. However this treatment option is generally possible in only 50-67% of patients who have meningeal hemangiopericytoma.

How is a meningeal solitary fibrous tumor diagnosed?

A meningeal solitary fibrous tumor (SFT)/hemangiopericytoma (HPC) is a diagnostic challenge due to its resemblance to more common brain tumors like meningioma, with histopathology being the definitive diagnostic test.  A 37-year-old male presented to our tertiary center with blurred vision, “not being himself,” and “acting funny” for three weeks.

Does radiotherapy protect against Neuraxis metastasis in intracranial meningeal hemangiopericytoma?

For patients with intracranial meningeal hemangiopericytoma, surgical removal followed by external radiotherapy reduced the risk of local recurrence. It was not demonstrated that postoperative radiotherapy protected against neuraxis metastasis.